Search on: THIAMINE TRIPHOSPHATE 
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Descriptor English:   Thiamine Triphosphate 
Descriptor Spanish:   Tiamina Trifosfato 
Descriptor Portuguese:   Tiamina Trifosfato 
Tree Number:   D02.886.675.900.900
D03.383.129.708.900.900
D03.383.742.795.900
Definition English:   3-((4-Amino-2-methyl-5-pyrimidinyl)methyl)-4-methyl-5-(4,6,8,8-tetrahydroxy-3,5,7-trioxa-4,6,8-triphosphaoct-1-yl)thiazolium hydroxide, inner salt, P,P',P''-trioxide. The triphosphate ester of thiamine. In Leigh's disease, this compound is present in decreased amounts in the brain due to a metabolic block in its formation. 
Indexing Annotation English:   do not confuse with THIAMIN TRIPHOSPHATASE; deficiency: coordinate THIAMINE TRIPHOSPHATE /defic (IM) with THIAMINE DEFICIENCY (IM)
Pharmacological Action:   Vitamin B Complex
 
History Note English:   91(79); was see under THIAMINE 1979-90 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AA analogs & derivatives
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DU diagnostic use EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UR urine
Record Number:   14216 
Unique Identifier:   D013838 

Occurrence in VHL:
 

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