Search on: HISTIDASE 
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Descriptor English:   Histidine Ammonia-Lyase 
Descriptor Spanish:   Histidina Amoníaco-Liasa 
Descriptor Portuguese:   Histidina Amônia-Liase 
Synonyms English:   Histidase  
Tree Number:   D08.811.520.232.400.500
Definition English:   An enzyme that catalyzes the first step of histidine catabolism, forming UROCANIC ACID and AMMONIA from HISTIDINE. Deficiency of this enzyme is associated with elevated levels of serum histidine and is called histidinemia (AMINO ACID METABOLISM, INBORN ERRORS). 
Indexing Annotation English:   /defic: consider also histidinemia (AMINO ACID METABOLISM, INBORN ERRORS)
History Note English:   98(73) 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DU diagnostic use DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   6797 
Unique Identifier:   D006638 

Occurrence in VHL:
 

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